Poland syndrome: from the perspective of invasive electrophysiology in a pediatric patient – A case report




Elibet Chávez-González, Electrophysiology Department, Cardiocentro Ernesto Guevara, Santa Clara, Cuba
Armando E. Hernández Castellón, Electrophysiology Department, Cardiocentro Ernesto Guevara, Santa Clara, Cuba
Fernando Rodríguez-González, Electrophysiology Department, Cardiocentro Ernesto Guevara, Santa Clara, Cuba
Juan M. Cruz-Elizundia, Electrophysiology Department, Cardiocentro Ernesto Guevara, Santa Clara, Cuba


Introduction: Poland syndrome is a rare congenital condition characterized by the unilateral absence or hypoplasia of the pectoralis major muscle, often with ipsilateral upper limb malformations. Cardiac displacement may complicate invasive procedures. Case report: A 15-year-old female with Poland syndrome and recurrent palpitations presented with documented atrioventricular nodal reentrant tachycardia (AVNRT). During the electrophysiological study, mesocardia altered expected catheter positions. Ablation was successfully performed under fluoroscopic guidance. Discussion: This case highlights the need to recognize anatomical variants in Poland syndrome when planning cardiac interventions. Successful ablation is feas



Keywords: Poland syndrome. Congenital cardiac displacement. Mesocardia. Pediatric arrhythmia. Radiofrequency catheter ablation. Case report.




Portuguese Journal of Pediatrics